AU - Bakhti, Souad AU - Tighilt, Nabila AU - Khoudir, Wahiba AU - Djennas, Mohamed TI - Iniencephaly with Long Survival: A Rare Condition PT - JOURNAL ARTICLE TA - IrJNS JN - IrJNS VO - 2 VI - 3 IP - 3 4099 - http://irjns.org/article-1-64-en.html 4100 - http://irjns.org/article-1-64-en.pdf SO - IrJNS 3 ABĀ  - Background & Importance: Iniencephaly is a rare cranio-cervical deformity. It belongs to neural tube defects. This disorder is characterized by a retroflexion of head, a very short neck, varying degrees of incomplete posterior closure of vertebrae and cervical and thoracic spinal synostosis. This malformation is associated with central nervous system and systemic malformations. Most of patients are dead born and others die after few hours of life. There are only few long-term survivors reported in literature. Case Presentation: A seven-year-old girl with iniencephaly signs who has been managed conservatively and still alive after six years of follow-up. Conclusion: Iniencephaly is a rare complexe disorder with a dismal prognosis but not uniformly fatal. CP - IRAN IN - * Corresponding Author Address: Place 1er Mai, Algiers, Algeria. Tel: +213661411881. Fax: +21323860025. Email: bak-sou@hotmail.com LG - eng PB - IrJNS PG - 19 PT - Case report YR - 2016