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Volume 2, Issue 3 (12-2016)
Iran J Neurosurg 2016, 2(3): 19-21 |
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Bakhti S, Tighilt N, Khoudir W, Djennas M. Iniencephaly with Long Survival: A Rare Condition. Iran J Neurosurg 2016; 2 (3) :19-21
URL: http://irjns.org/article-1-64-en.html
URL: http://irjns.org/article-1-64-en.html
1- Professor, Pediatric Neurosurgery Division, Mustapha Pacha University Hospital, Algiers, Algeria
2- Assistant Professor, Pediatric Neurosurgery Division, Mustapha Pacha University Hospital, Algiers, Algeria
3- Consultant in Neurosurgery, Department of Neurosurgery, Mustapha Pacha University Hospital, Algiers, Algeria
4- Professor, Chief Department of Neurosurgery, Mustapha Pacha University Hospital, Algiers, Algeria
2- Assistant Professor, Pediatric Neurosurgery Division, Mustapha Pacha University Hospital, Algiers, Algeria
3- Consultant in Neurosurgery, Department of Neurosurgery, Mustapha Pacha University Hospital, Algiers, Algeria
4- Professor, Chief Department of Neurosurgery, Mustapha Pacha University Hospital, Algiers, Algeria
Abstract: (5582 Views)
Background & Importance: Iniencephaly is a rare cranio-cervical deformity. It belongs to neural tube defects. This disorder is characterized by a retroflexion of head, a very short neck, varying degrees of incomplete posterior closure of vertebrae and cervical and thoracic spinal synostosis. This malformation is associated with central nervous system and systemic malformations. Most of patients are dead born and others die after few hours of life. There are only few long-term survivors reported in literature.
Case Presentation: A seven-year-old girl with iniencephaly signs who has been managed conservatively and still alive after six years of follow-up.
Conclusion: Iniencephaly is a rare complexe disorder with a dismal prognosis but not uniformly fatal.
Type of Study: Case report |
Subject:
Gamma Knife Radiosurgery
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This is an open access article distributed under the terms of the Creative Commons Attribution License (CC-By-NC), which permits use, distribution, and reproduction in any medium, provided the original work is properly cited and is not used for commercial purposes.
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